Understanding Prader-Willi Syndrome: A Quizlet


Презентация на тему "TOPIC Human hereditary diseases. Chromosomal
Презентация на тему "TOPIC Human hereditary diseases. Chromosomal from www.myshared.ru

Introduction

Prader-Willi Syndrome (PWS) is a rare genetic disorder that affects about 1 in every 15,000 births. PWS is caused by a deletion or lack of expression of certain genes on chromosome 15. This can lead to various physical, cognitive, and behavioral issues. In this quizlet, we will explore the different aspects of PWS.

Physical Symptoms

One of the most prominent symptoms of PWS is hyperphagia, which is an insatiable appetite that can lead to obesity. Other physical symptoms include short stature, hypotonia (low muscle tone), and small hands and feet. Individuals with PWS may also have scoliosis, sleep apnea, and dental issues.

Cognitive Symptoms

Individuals with PWS may have intellectual disabilities ranging from mild to moderate. They may also struggle with executive functioning skills, such as planning and organizing. However, some individuals with PWS have average intelligence and can lead independent lives with proper support.

Behavioral Symptoms

Individuals with PWS may exhibit challenging behaviors, such as temper tantrums, stubbornness, and obsessive-compulsive behaviors. They may also have difficulty with social skills and may struggle with understanding social cues and norms. However, with proper interventions, these behaviors can be managed.

Diagnosis

PWS can be diagnosed through genetic testing, which looks for the deletion or lack of expression of genes on chromosome 15. Prenatal testing is also available for families with a history of PWS. Early diagnosis is critical for proper treatment and support.

Treatment

There is currently no cure for PWS, but early intervention and management can improve outcomes. Treatment may include growth hormone therapy to improve height, behavioral therapy to address challenging behaviors, and a strict, controlled diet to manage hyperphagia and obesity.

Support and Resources

Families of individuals with PWS may benefit from support groups and organizations, such as the Prader-Willi Syndrome Association. These organizations provide resources, education, and advocacy for individuals with PWS and their families.

Conclusion

Prader-Willi Syndrome is a complicated disorder that affects various aspects of an individual's life. However, with proper support and management, individuals with PWS can lead fulfilling lives. Early diagnosis and intervention are critical for improving outcomes.

Sources:

- Prader-Willi Syndrome Association - National Organization for Rare Disorders - Genetics Home Reference

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